Most people need surgery to remove the tumor. Primary cardiac tumors are rare entities, and the majority of these are benign In adults, papillary fibroelastomas (pfes) and cardiac myxomas are the most common types of primary cardiac tumors Papillary fibroelastoma is a benign neoplasm A single large series of 511 patients at mayo clinic by tamin et al Reported pfes as the most common cardiac tumor [1]
A papillary fibroelastoma is a primary tumor of the heart that typically involves one of the heart valves [1] papillary fibroelastomas, while considered uncommon, make up about 10 percent of all primary tumors of the heart [2] they are the third most common type of primary tumor of the heart, [3] behind cardiac myxomas and cardiac lipomas. (a and b) aortic valve zoom at 141° At the aortic face and free edge of the left coronary cusp, a heterogeneous mass of 12 × 4 mm with irregular edges, mobile and flaming, pedicled with multiple terminal digitiform branches that resemble a sea anemone was visualized, which very probably corresponds to a papillary fibroelastoma (pfe) (video 1). Papillary fibroelastomas are rare benign primary cardiac tumors
When papillary fibroelastoma was a secondary indication for surgery (158 patients, 54%), the lesion was identified preoperatively in 39% Papillary fibroelastomas were located most commonly on the aortic valve and least commonly in the right side of the heart. Papillary fibroelastomas undergo surgical excision because of their (thrombo) embolic potential The most common mechanism is thought to be related to thrombus formation with subsequent embolization However, portions of the tumor may fragment and result in downstream ischemia. Background papillary fibroelastoma (pfe) is a rare, benign cardiac tumor that most commonly involves the heart valves, particularly the aortic valve
Although often asymptomatic, pfes can lead to serious complications such as embolic or ischemic events This case highlights an atypical presentation of pfe in a young patient, emphasizing the diagnostic and management challenges encountered.
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